Abstract:
Ewing sarcoma is a relatively uncommon malignant bone
neoplasm that usually occurs in children and young
adults and involves the major long bones, pelvis, and
ribs. Primary diaphragmatic Ewing sarcoma is extremely
rare. To the best of our knowledge, only three cases of
primary Ewing sarcoma of the diaphragm have been
reported. A 12-year-old girl presented spontaneous occurrences of the right hemothorax. After drainage, a
roentgenogram film, computed tomography, ultrasonography, and magnetic resonance image showed a giant
mass on the right diaphragm. Primary diaphragmatic
tumor was resected totally by right posterolateral thoracotomy, and histologically, an extraskeletal Ewing sarcoma was identified. The patient received adjuvant radiochemotherapy, and there was no evidence of disease 10
months after the operation. Although extremely rare,
extraskeletal Ewing sarcoma should be kept in mind in
the differential diagnosis of diaphragmatic soft tissue
tumors.
